Williams-Campbell syndrome is a cystic bronchiectatic disease secondary to deficiency or defect of cartilaginous plates in the wall of the airways. In the literature, two main forms are suggested: congenital and acquired (post-infectious). The most frequent symptoms are represented by recurrent pulmonary infections from childhood. Multislice spiral dynamic CT has a major role in the study of cystic pulmonary disease and in differentiating Williams-Campbell syndrome from the other causes of cystic bronchiectasis, in which even lung function tests can give deceptive results.
The role of spiral multidetector dynamic CT in the study of Williams-Campbell syndrome / Di Scioscio, Valerio; Zompatori, Maurizio; Mistura, Isabella; Montanari, Paolo; Santilli, Lucia; Luccaroni, Roberta; Sverzellati, Nicola. - In: ACTA RADIOLOGICA. - ISSN 0284-1851. - 47(2006), pp. 798-800. [10.1080/02841850600849084]